英四歲小孩大腦分泌致命毒素 活不過十歲
Distraught parents have told how their son is slowly being poisoned by his own brain.
Blighted by a fatal neurological disorder, four-year-old Morgan Mawson is unlikely to make it to his tenth birthday and is unable to walk or talk.
He is one of 200 children in the UK who have infantile Batten's disease which is so rare his parents' chance of meeting and conceiving him was only one in two billion.
Both Jenni, 28, and Eddie, 37, from Derby are carriers of the faulty gene which causes Batten's disease - meaning any of their children have a one in four chance of inheriting the condition.
At birth there are no symptoms of the disorder so it was only when Morgan failed to develop properly that his parents realised there was something wrong.
Doctors told the devastated couple that he was not expected to reach his tenth birthday and that a deadly bodily poison was slowly destroying his brain.
Jenni said: “His brain produces a chemical which can be poisonous but Morgan is missing an enzyme which dissolves it - so that poison is killing off his brain.”
“It's killing off his nerves in his arms, legs and mouth - it stops him from being able to chew and talking properly.”
“His behaviour is regressing. At the moment he wants to throw things everywhere and he wants to put things in his mouth. It's like we've gone back to the baby stage.”
Eddie and Jenni have had to quit their jobs to act as full time carers for their children.據英國《每日郵報》11月9日報道，一對傷心欲絕的父母講述了他們的兒子是如何被自己的大腦慢慢毒害的。
4歲的摩根-莫森身患一種致命的神經性疾病，他不大可能會度過自己的第十個生日，並且無法行走或說話。
他是英國200個患有嬰兒貝敦氏症的小孩之一。這種疾病十分罕見， 罹患它的可能性只有二百萬分之一。
來自英國德比郡的28歲的珍妮與37歲的艾迪都攜帶有能導致貝敦氏症的錯誤基因，這就意味着他們任何一個孩子都有四分之一遺傳這種基因的機會。
摩根出生時身體並未出現任何紊亂症狀，所以只有當他未能正常發育時他的父母才意識到出了問題。
醫生告訴這對倍感震驚的夫婦，摩根預計活不過十歲。一種致命的身體毒素正慢慢地破壞他的大腦。
珍妮說：“他的大腦分泌出了一種有毒的化學物質，但是摩根身體裏卻沒有能夠分解它的酶。所以該毒素正在殺死他的大腦。”
“這種毒素正在殺死他的手臂、腿部和嘴部的神經，那將會阻礙摩根正常的咀嚼和講話。”
“他的言行正在倒退。現在他想要四處亂丟東西，並且想往嘴巴里塞東西。他就像回到了嬰兒階段。”
艾迪和珍妮已經不得不辭去工作在家全職照看他們的孩子。
